Incontinentia Pigmenti

• Incontinentia Pigmenti Overview
• Incontinentia Pigmenti Causes
• Incontinentia Pigmenti Symptoms
• When to Seek Medical Care
• Exams and Tests
• Incontinentia Pigmenti Treatment
• Medical Treatment
• Next Steps
• Prevention
• Outlook
• For More Information
• Web Links
• Multimedia
• Synonyms and Keywords
• Authors and Editors

Incontinentia Pigmenti Overview

Incontinentia pigmenti, sometimes referred to as IP or Bloch-Sulzberger syndrome, is an unusual inherited disorder of skin pigmentation that is associated with abnormalities of the skin (100% of affected people), teeth (90% of affected people), bones (40% of affected people), brain or spinal cord (40% of affected people), and eyes (35% of affected people). The exact cause of IP is not yet known.

Incontinentia pigmenti is often diagnosed in affected people when they are newborns because of the presence of a characteristic rash. The skin changes often disappear with time, but an evaluation for nervous system and eye disturbances must be promptly initiated.