Incontinentia Pigmenti (cont.)
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Outlook
Although retinal detachment occurs only in a minority of babies with IP, this is a serious abnormality that can lead to blindness during their first few months of life. An individual's overall prognosis varies depending on the degree of visual impairment and nervous system involvement.
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Incontinentia Pigmenti »
Incontinentia pigmenti (IP) is an X-linked dominant neurocutaneous syndrome with cutaneous, neurologic, ophthalmologic, and dental manifestations.
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