Definition of Stargardt diseaseStargardt disease: An hereditary eye disease that is one of the most frequent causes of macular degeneration in childhood. (The macula is the part of the retina that is responsible for central vision.) Source: MedTerms™ Medical Dictionaryhttp://www.medterms.com/script/main/art.asp?articlekey=13005 Last Editorial Review: 10/9/2012
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