Definition of IsodisomyIsodisomy: A remarkable situation in which both chromosomes in a pair are from one parent only. Isodisomy causes some birth defects and is suspected to play a role in cancer. Also known as uniparental disomy. Source: MedTerms™ Medical Dictionaryhttp://www.medterms.com/script/main/art.asp?articlekey=4056 Last Editorial Review: 3/19/2012
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